Mice that lack activity of alphavbeta6- and alphavbeta8-integrins reproduce the abnormalities of Tgfb1- and Tgfb3-null mice

J Cell Sci. 2009 Jan 15;122(Pt 2):227-32. doi: 10.1242/jcs.035246.

Abstract

The arginine-glycine-aspartate (RGD)-binding integrins alphavbeta6 and alphavbeta8 activate latent TGFbeta1 and TGFbeta3 in vivo, but it is uncertain whether other RGD-binding integrins such as integrins alphavbeta5 and alphavbeta3 activate these TGFbeta isoforms. To define the combined role of alphavbeta6- and alphavbeta8-integrin in TGFbeta activation, we analyzed mice lacking function of both integrins by means of gene deletion and/or pharmacologic inhibition. Most Itgb6-/-;Itgb8-/- embryos die at mid-gestation; those that survive develop cleft palate-as observed in Tgfb3-/- mice. Itgb8-/- mice treated with an anti-alphavbeta6-integrin antibody develop severe autoimmunity and lack Langerhans cells-similar to Tgfb1-null mice. These results support a model in which TGFbeta3-mediated palate fusion and TGFbeta1-mediated suppression of autoimmunity and generation of Langerhans cells require integrins alphavbeta6 and alphavbeta8 but not other RGD-binding integrins as TGFbeta activators.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antigens, Neoplasm / genetics
  • Antigens, Neoplasm / immunology
  • Antigens, Neoplasm / metabolism*
  • Autoimmunity / genetics
  • Autoimmunity / immunology
  • Cleft Palate / genetics
  • Cleft Palate / immunology
  • Cleft Palate / metabolism*
  • Integrins / genetics
  • Integrins / immunology
  • Integrins / metabolism*
  • Kaplan-Meier Estimate
  • Langerhans Cells / immunology
  • Mice
  • Mice, Knockout
  • Oligopeptides / metabolism
  • Palate / abnormalities*
  • Palate / immunology
  • Palate / metabolism
  • T-Lymphocytes, Regulatory / immunology
  • T-Lymphocytes, Regulatory / metabolism
  • Transforming Growth Factor beta1 / genetics
  • Transforming Growth Factor beta1 / immunology
  • Transforming Growth Factor beta1 / metabolism*
  • Transforming Growth Factor beta3 / genetics
  • Transforming Growth Factor beta3 / immunology
  • Transforming Growth Factor beta3 / metabolism*

Substances

  • Antigens, Neoplasm
  • Integrins
  • Oligopeptides
  • Transforming Growth Factor beta1
  • Transforming Growth Factor beta3
  • integrin alphavbeta6
  • integrin alphavbeta8
  • arginyl-glycyl-aspartic acid