RecName: Full=2-oxoisovalerate dehydrogenase subunit beta, mitochondri - Protein

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Successful treatment of severe MSUD in Bckdhb(-/-) mice with neonatal AAV gene therapy. [J Inherit Metab Dis. 2024]
Successful treatment of severe MSUD in Bckdhb(-/-) mice with neonatal AAV gene therapy.
Pontoizeau C, Gaborit C, Tual N, Simon-Sola M, Rotaru I, Benoist M, Colella P, Lamazière A, Brassier A, Arnoux JB, et al. J Inherit Metab Dis. 2024 Jan; 47(1):41-49. Epub 2023 Mar 15.
Molecular cloning and analysis of the expression of the E1 beta subunit of branched chain alpha-ketoacid dehydrogenase in mice. [Biochim Biophys Acta. 1993]
Molecular cloning and analysis of the expression of the E1 beta subunit of branched chain alpha-ketoacid dehydrogenase in mice.
Chinsky JM, Costeas PA. Biochim Biophys Acta. 1993 Dec 14; 1216(3):499-503.
Mild inborn errors of metabolism in commonly used inbred mouse strains. [Mol Genet Metab. 2019]
Mild inborn errors of metabolism in commonly used inbred mouse strains.
Leandro J, Violante S, Argmann CA, Hagen J, Dodatko T, Bender A, Zhang W, Williams EG, Bachmann AM, Auwerx J, et al. Mol Genet Metab. 2019 Apr; 126(4):388-396. Epub 2019 Jan 24.

RefSeq protein isoforms
See 5 reference sequence protein isoforms for the Bckdhb gene.

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Mouse Genome Informatics (MGI) [Mouse Genome Informatics (MGI)]
Mouse Genome Informatics (MGI)
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reagents
ExactAntigen/Labome

RecName: Full=2-oxoisovalerate dehydrogenase subunit beta, mitochondrial; AltNam...
RecName: Full=2-oxoisovalerate dehydrogenase subunit beta, mitochondrial; AltName: Full=Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; Short=BCKDE1B; Short=BCKDH E1-beta; Flags: Precursor
gi|162416262|sp|Q6P3A8.2|ODBB_MOUSE

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